A 6-year-old boy presents with early pubic hair development and accelerated linear growth. Vital signs show BP 148/92 mmHg, HR 88/min, RR 18/min, temperature 37°C. Laboratory studies reveal low cortisol (3 μg/dL), suppressed plasma renin activity, and markedly elevated DHEA-S (580 μg/dL). Serum glucose is normal. Abdominal imaging shows no masses. Which enzyme deficiency best explains these findings?

  1. A)21 hydroxylase
  2. B)17 alpha hydroxylase
  3. C)5 alpha reductase
  4. D)11 beta hydroxylaseGABARITO
  5. E)Aldosterone synthase

Explicação

11 beta hydroxylase deficiency decreases cortisol synthesis and diverts precursors toward androgen production, causing precocious puberty or virilization. Deoxycorticosterone accumulates upstream and acts as a mineralocorticoid, producing hypertension and low ... Ver explicação completa e trilha adaptativa →

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