A 19-year-old woman presents to her neurologist 6 weeks after starting valproic acid for newly diagnosed idiopathic generalized epilepsy. She reports tremor, progressive weight gain of 8 pounds over this period, and diffuse hair loss. She also notes that her menstrual period has not occurred in the past 2 months. Vital signs are stable with BP 118/76 mmHg, HR 88 bpm, RR 16/min, and temperature 37.2°C. Laboratory studies show: serum ammonia 95 μmol/L (normal <50), AST 28 U/L, ALT 31 U/L, total bilirubin 0.8 mg/dL, TSH 2.1 mIU/L. Which of the following best explains her clinical presentation?

  1. A)Hepatotoxicity with acute liver failure requiring immediate medication discontinuation
  2. B)Hypothyroidism secondary to valproic acid metabolism of thyroid hormone
  3. C)Hyperammonemia with secondary amenorrhea and endocrine dysfunctionGABARITO
  4. D)Teratogenic effects of valproic acid manifesting as congenital abnormalities
  5. E)Drug-induced systemic lupus erythematosus with multi-organ involvement

Explicação

Valproic acid is well-known for causing hyperammonemia through inhibition of the urea cycle and carbamoyl phosphate synthetase. The elevated ammonia (95 μmol/L, well above normal) directly causes neurological symptoms (tremor) and metabolic effects. Additional... Ver explicação completa e trilha adaptativa →

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