A 45-year-old woman presents to clinic with a 10-year history of primary biliary cholangitis (PBC) diagnosed by positive anti-mitochondrial antibody and liver biopsy. She reports progressive fatigue, pruritus, and jaundice over the past 6 months. She has been compliant with ursodeoxycholic acid (UDCA) 13-15 mg/kg/day for 8 years. Current laboratory values show: alkaline phosphatase 280 U/L (normal <120), gamma-glutamyl transferase 320 U/L (normal <55), total bilirubin 2.8 mg/dL (normal <1.2), ALT 35 U/L (normal <40), and AST 42 U/L (normal <40). Abdominal ultrasound shows no evidence of portal hypertension or cirrhosis. Which of the following is the most appropriate next pharmacologic intervention to slow disease progression?

  1. A)Prednisolone 20 mg daily
  2. B)Azathioprine 50 mg daily
  3. C)Methotrexate 15 mg weekly
  4. D)Obeticholic acid (farnesoid X receptor agonist)GABARITO
  5. E)Infliximab 5 mg/kg intravenously

Explicação

Obeticholic acid is a farnesoid X receptor (FXR) agonist that is indicated as second-line therapy for PBC patients with an inadequate response to UDCA monotherapy. This patient demonstrates inadequate response to UDCA (persistent elevation of alkaline phosphat... Ver explicação completa e trilha adaptativa →

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