A 45-year-old man with diabetes mellitus type 2 presents with recurrent pancreatitis. Laboratory studies show triglycerides of 1,200 mg/dL and total cholesterol of 680 mg/dL. His father died of myocardial infarction at age 52. Genetic testing reveals a mutation in the lipoprotein lipase gene. Which of the following pathways is primarily impaired in this patient?

  1. A)Synthesis of apolipoprotein B-100 in hepatocytes
  2. B)Uptake of LDL particles via LDL receptor-mediated endocytosis
  3. C)Hydrolysis of triglycerides in chylomicrons and VLDL by lipoprotein lipaseGABARITO
  4. D)Esterification of cholesterol in HDL by LCAT
  5. E)Conversion of VLDL to IDL by hepatic triglyceride lipase

Explicação

Lipoprotein lipase (LPL) deficiency causes Type I hyperlipoproteinemia with severe hypertriglyceridemia due to accumulation of chylomicrons and VLDL. LPL is the enzyme responsible for hydrolysis of triglycerides in these lipoproteins at the capillary endotheli... Ver explicação completa e trilha adaptativa →

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