A 45-year-old man presents with xanthomas on his Achilles tendons and eyelids, along with corneal arcus. Laboratory studies show total cholesterol of 650 mg/dL and LDL of 520 mg/dL despite dietary modification. His father died of myocardial infarction at age 52. Which of the following genetic mutations is most likely responsible for this condition?

  1. A)Loss-of-function mutation in CETP
  2. B)Gain-of-function mutation in PCSK9
  3. C)Mutation in the apoB-100 binding domain
  4. D)Deficiency of lipoprotein lipase
  5. E)Loss-of-function mutation in the LDL receptor geneGABARITO

Explicação

This patient has familial hypercholesterolemia (FH) with premature coronary disease and xanthomas. The classic presentation of heterozygous FH results from loss-of-function mutations in the LDL receptor gene, leading to impaired hepatic uptake of LDL particles... Ver explicação completa e trilha adaptativa →

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