A 3-day-old newborn presents with cyanosis and severe respiratory distress. Vital signs show HR 168 bpm, RR 52/min, BP 55/32 mmHg, SpO2 78% on room air, and temperature 37.2°C. Echocardiography demonstrates complete transposition of the great arteries with the aorta arising anteriorly from the right ventricle and the pulmonary artery from the left ventricle. Chest X-ray shows an "egg-on-string" appearance. There is no evidence of septal defects. Which embryologic process is most likely disrupted?

  1. A)Incomplete resorption of septum primum
  2. B)Premature closure of foramen ovale
  3. C)Abnormal truncus arteriosus septationGABARITO
  4. D)Defective endocardial cushion development
  5. E)Failure of neural crest cell migration

Explicação

Transposition of the great arteries results from abnormal division and rotation of the truncus arteriosus by the aorticopulmonary septum during weeks 4-6 of development. Improper spiraling of this septum causes the vessels to switch their normal connections to... Ver explicação completa e trilha adaptativa →

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