A 2-day-old male infant born at 39 weeks gestation presents with progressive cyanosis and respiratory distress. Vital signs show SpO2 of 28% on room air, heart rate 168 bpm, respiratory rate 62/min, and blood pressure 58/35 mmHg. Physical examination reveals a single loud S2 and no significant murmur. Chest X-ray shows cardiomegaly with a narrow mediastinum and increased pulmonary vascular markings. Echocardiography demonstrates a single arterial trunk originating from the heart that gives rise to the pulmonary arteries, aorta, and coronary arteries, with a large ventricular septal defect. The infant has not received prostaglandin E1. Which of the following is the most likely diagnosis?
- A)Transposition of the great arteries with an atrial septal defect
- B)Total anomalous pulmonary venous return
- C)Tetralogy of Fallot with coronary artery anomaly
- D)Pulmonary atresia with intact ventricular septum
- E)Truncus arteriosusGABARITO
Explicação
Truncus arteriosus is characterized by a single arterial trunk arising from the heart that supplies the systemic, pulmonary, and coronary circulations, with an obligatory ventricular septal defect. The pathophysiology involves failure of the embryologic truncu... Ver explicação completa e trilha adaptativa →